English Translation, Synonyms, Definitions and Usage Examples of Spanish Word ‘enfermedad de Degos’. Meanings of “enfermedad de degos” in English Spanish Dictionary: 1 result(s) Meanings of “enfermedad de degos” with other terms in English Spanish. Me llamo Loli tengo 37 aƱos y vivo en Madrid y me diagnoticaron la enfermedad de Degos en despues de que perdiera la vision del ojo.

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Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. A clinical inspection of the skin should be combined with additional examinations including brain magnetic resonance tomography, gastroscopy, colonoscopy, X-ray of the chest and ennfermedad ultrasound, in order to assess the long-term prognosis. Etiology The etiopathogenesis of the disease remains unknown.

Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions. Genetic counseling A genetic predisposition with an autosomal dominant trait has been enfrmedad. Continuing navigation will be considered as acceptance of this use. Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. You can change the settings or obtain more information by clicking here.

Go to the members area of the website of the AEDV, https: Later a wedge-shaped connective tissue necrosis in the deep dermis, due to a thrombotic occlusion of the small arteries and sparse lymphocytes, occurs. CiteScore measures average citations received per document published.

enfermedad de Degos – English Translation – Word Magic Spanish-English Dictionary

Check this box if you wish to receive a copy of your message. Systemic manifestations are progressive and may lead to serious complications: Disease definition Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim.

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All enfermead are subjected to a rigorous process of revision in pairs, and careful editing for literary and scientific style. Print Send to a friend Export reference Mendeley Statistics. Health care resources for this disease Expert centres 69 Diagnostic tests 0 Patient organisations 21 Orphan drug s 0. The etiopathogenesis of the disease remains unknown. Clinical description MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities.

For all other comments, please send your remarks via contact us. This item has received. Over several days, the center of the lesions sinks and develops a characteristic morphology: The material is in no way intended to replace professional medical care by endermedad qualified specialist and should not be used as a basis for diagnosis or treatment.

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Previous article Next article. Face, scalp, palms of hands and soles of feet are rarely involved. No effective treatment for the systemic manifestations has been established, however, subcutaneous treprostinil has dehos tested successfully in one case with intestinal and CNS manifestations.

Diagnosis is based primarily on the cutaneous clinical picture that is nearly pathognomonic. Other search option s Alphabetical list.

In early stages, histology of lesions may reveal a superficial and deep perivascular lymphocytic infiltration with distinct mucin deposition. More developed lesions show prominent changes in the dermoepidermal junction, with atrophy of the epidermis and an area of sclerosis in the papillary dermis.

Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases. It may more rarely manifest as pericarditis or in other organs such as the lungs, presenting as pleuritis. Additional information Further information on this disease Classification s 3 Gene s 0 Clinical signs and symptoms Degod in PubMed Other website s 7.

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If you are a member of the AEDV: Si continua navegando, consideramos que acepta su uso. More developed lesions can imitate lichen sclerosus see this term. Are you dnfermedad health professional able to prescribe or dispense drugs?

Orphanet: Enfermedad de Degos

May Pages ee22 Pages As all patients may potentially develop the systemic, life-threatening variant, an annual follow-up is mandatory. Only comments written in English can be processed.

Many patients have been reported to have defects in blood coagulation. From Monday to Friday from 9 a. Pemphigus Vegetans in the Inguinal Folds. Diagnostic methods Diagnosis is based primarily on the cutaneous clinical picture that is nearly pathognomonic. SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s impact.

Subscribe to our Newsletter. Summary and related texts. In the year has been indexed in the Medlinedatabase, and has become a vehicle for expressing the most current Spanish medicine and ce.

Differential diagnosis The histology of early lesions resembles cutaneous lupus erythematosus see this term. Hypotheses implicating vasculitis, coagulopathy or a primary dysfunction of endothelial cells have been proposed.

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Systemic lesions may affect the gastrointestinal tract and the central nervous system CNS and are potentially lethal.